Isolated left ventricular noncompaction causing refractory heart failure
نویسندگان
چکیده
منابع مشابه
Isolated left ventricular noncompaction syndrome.
Isolated left ventricular noncompaction (ILVNC) is a rare congenital cardiomyopathy characterized by prominent trabeculae, deep intertrabecular recesses, and thickened myocardium with 2 distinct layers (compacted and noncompacted). Clinical characteristics, outcomes, and appropriate therapies remain poorly defined. Data were collected on patients diagnosed with ILVNC by echocardiographic criter...
متن کاملIsolated Noncompaction of Left Ventricular Myocardium
Isolated noncompaction of left ventricular myocardium is a rare disorder of endomyocardial morphogenesis characterized by numerous, excessively prominent ventricular trabeculations and deep intertrabecular recesses. This study comprised eight cases, including three at necropsy. Ages ranged from 11 months to 22.5 years, with follow-up as long as 5 years. Gross morphological severity ranged from ...
متن کاملEchocardiographic characteristics of isolated left ventricular noncompaction
BACKGROUND Although isolated left ventricular noncompaction (ILVNC) has been described almost two decades ago, our knowledge about its diagnosis, presentation, echocardiographic features and clinical outcome is sparse. We aimed to assess the echocardiographic and clinical characteristics of ILVNC in a group of patients referred to our center. METHODS Patients who were referred to a tertiary r...
متن کاملIsolated left ventricular noncompaction as a cause for heart failure and heart transplantation: a single center experience.
OBJECTIVES To determine the prevalence of isolated left ventricular noncompaction (IVNC) as a cause of heart failure and heart transplantation. METHODS There were 960 patients seen in the heart failure clinic from 1987 to 2005, with a complete evaluation including echocardiography at our center (study population, 82% men, mean age 52 years). The following data were collected: type of heart di...
متن کاملLeft Ventricular Noncompaction
Ma Whether left ventricular noncompaction (LVNC) is a distinct cardiomyopathy or a morphologic trait shared by different cardiomyopathies remains controversial. Current guidelines from professional organizations recommend different strategies for diagnosing and treating patients with LVNC. This state-of-the-art review discusses new insights into the basic mechanisms leading to LVNC, its clinica...
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ژورنال
عنوان ژورنال: Revista Portuguesa de Cardiologia (English Edition)
سال: 2016
ISSN: 2174-2049
DOI: 10.1016/j.repce.2015.09.014